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Complete Common Atrioventricular Canal Defect, also known as Atrioventricular Septal Defect, is a lack of separation of the atria and the ventricles into separate right and left chambers as well as a lack of separation of the mitral and tricuspid valves. The lack of separation of these two valves results in a single atrioventricular valve.
In patients with atrioventricular canal defect, the single atrioventricular may not close properly. Therefore, the heart must pump an excessive amount of blood and this may result in an enlargement of the heart.
Surgical repair for atrioventricular canal defect is required within the first six months of life. The surgery involves sewing patches over the ASD and VSD and carefully separating the single atrioventricular valve into two valves.
How Does Atrioventricular Canal Defect Differ From
Normal Cardiac Anatomy?
If your child has atrioventricular canal defect the structure of his or her heart is different from normal cardiac anatomy.
Heart With Normal Cardiac Anatomy
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Adobe Flash Player.
When your child has a congenital heart defect, there's usually something wrong with the structure of his or her heart's structure.
The heart is composed of four chambers. The two upper chambers, known as atria, collect blood as it flows back to the heart. The two lower chambers, known as ventricles, pump blood with each heartbeat to the two main arteries (the pulmonary artery and the aorta). The septum is the wall that divides the heart into right and left sides. The atrial septum separates the right and left atria; likewise, the ventricular septum separates the two ventricles.
There are four valves that control the flow of blood through the heart. These flap-like structures allow blood to flow in only one direction. The tricuspid and mitral valves, also known as the atrioventricular valves, separate the upper and lower chambers of the heart. The aortic and pulmonary valves, also known as the arterial valves, separate the ventricles from the main arteries. Oxygen-depleted blood returns from the body and drains into the right atrium via the superior and inferior vena cavas. The blood in the right atrium then passes through the tricuspid valve and enters the right ventricle.
Next, the blood passes through the pulmonary valve, enters the pulmonary artery, and travels to the lungs where it is replenished with oxygen. The oxygen-rich blood returns to the heart via the pulmonary veins, draining into the left atrium. The blood in the left atrium passes through the bicuspid, or mitral, valve and enters the left ventricle.
Finally, the oxygen-rich blood flows through the aortic valve into the aorta and out to the rest of the body.
From Nemours' KidsHealth
- ECG (Electrocardiogram)
- Cardiac Catheterization
- Congenital Heart Defects
- When Your Child Needs a Heart Transplant
- Congenital Heart Defects
- Coarctation of the Aorta
- Atrial Septal Defect
- Tetralogy of Fallot
- Patent Ductus Arteriosus (PDA)
- Heart and Circulatory System
- Ventricular Septal Defect
- A to Z: Atrial Flutter
- A to Z: Patent Ductus Arteriosus (PDA)
- Heart Murmurs
- A to Z: Tetralogy of Fallot
- Congenital Heart Defects Special Needs Factsheet
- A to Z: Hypoplastic Left Heart Syndrome
Trusted External Resources
Congenital Heart Defects Special Needs Factsheet
What Teachers Should Know
Congenital heart defects develop in fetuses early in pregnancy, causing one abnormality or a combination of abnormalities in the structure of the heart. Some of the more common defects are:
- holes in the walls between the heart's chambers
- abnormal heart valves
- abnormalities in the blood vessels entering or leaving the heart
Congenital heart defects can range from mild to severe. Some may cause serious symptoms at birth, requiring intensive hospital care. Other defects may not be diagnosed until the teen or even adult years.
Most kids and teens with simple heart defects don't need any special care at school. Those with more complicated heart defects, though, may show signs that need attention, such as:
- fast breathing or shortness of breath
- bluish coloring of the skin (cyanosis)
- chest discomfort
Students with congenital heart defects may:
- tire easily or want to avoid activities that require a lot of exertion
- have activity restrictions
- need to carry a water bottle to stay hydrated or stay indoors on hot days
- need extra time to go to and from classes
- need to go the bathroom a lot if they're taking diuretic medication
- have bluish skin coloring due to low oxygen levels
- need to use supplemental oxygen
- need to go to the school nurse for medicines
- miss class time to see cardiologists or other medical professionals
- have developmental delays or learning problems
What Teachers Can Do
Check with your student's parents or guardians to learn about the nature of the heart condition and any effects on learning and school activities.
If a student with a congenital heart defect misses class time for doctor visits or hospitalizations, allow extra time for assignments and provide make-up work if appropriate. Most kids and teens with congenital heart defects can fully participate in most physical and extracurricular activities and should be encouraged to do so.
Reviewed by: Mary L. Gavin, MD
Date reviewed: June 01, 2018